Part 1 Brain

Section 1 Disorders of Brain Development

Subsection 1.1 Disorders of Neural Tube Closure and Diverticulation

1 Anencephaly

2 Cephalocele

3 Atretic Cephalocele

4 Holoprosencephaly


Subsection 1.2 Disorders of Corpus Callosum and Septum Pellucidum

5 Agenesis of Corpus Callosum

6 Septo-optic Dysplasia

7 Cavum Septi Pellucidi and Cavum Vergae


Subsection 1.3 Disorders of Neuronal Migration

8 Lissencephaly

9 Polymicrogyria

10 Gray Matter Heterotopia

11 Schizencephaly


Subsection 1.4 Chiari Malformation

12 Chiari I Malformation

13 Chiari II Malformation


Subsection 1.5 Disorders of the Posterior Fossa

14 Rhombencephalosynapsis

15 Joubert Malformation

16 Dandy-Walker Malformation

17 Mega Cisterna Magna


Subsection 1.6 Disorders of the Pituitary Gland

18 Pituitary Aplasia

19 Pituitary Duplication

20 Posterior Pituitary Ectopia


Subsection 1.7 Miscellaneous Disorders

21 Persistent Open Anterior Fontanelle

22 Porencephaly

23 Hydranencephaly

24 Optic Nerve Hypoplasia


Section 2 Disorders of the Perinatal Period

25 Cephalhematoma

26 Caput Succedaneum and Germinal Matrix Hemorrhage

27 Periventricular Leukomalacia

28 Hypoxic-Ischemic Encephalopathy

29 Kernicterus

30 TORCH infections


Section 3 Metabolic and Neurodegenerative Diseases of Childhood

Subsection 3.1 Gray Matter Disorders

31 Hallervorden-Spatz Disease

32 Infantile Neuroaxonal Dystrophy


Subsection 3.2 White Matter Disorders

33 Alexander's Disease

34 Canavan Disease

35 Pelizaeus-Merzbacher Disease


Subsection 3.3 Inborn Errors of Intermediary Metabolism

36 Propionic Acidemia

37 Glutaric Aciduria Type 1


Subsection 3.4 Lysosomal Diseases

38 Fabry Disease

39 Metachromatic Leukodystrophy

40 Krabbe Disease

41 Mucopolysaccharidoses


Subsection 3.5 Mitochondrial Diseases &' 'amp; Peroxisomal Diseases

42 Kearns-Sayre Syndrome

43 MELAS

44 Leigh Syndrome

45 Classic X-linked Adrenoleukodystrophy


Section 4 Phakomatoses/Neurocutaneous syndromes

46 Neurofibromatosis Type 1

47 Neurofibromatosis Type 2

48 Tuberous Sclerosis

49 Sturge-Weber Syndrome

50 Von Hippel-Lindau Syndrome

51 Ataxia Telangiectasia

52 Neurocutaneous Melanosis



Section 5 Seizures

53 Mesial Temporal Sclerosis

54 Hemimegalencephaly

55 Focal Cortical Dysplasia of Taylor

56 Epileptogenic Focus

57 Status Epilepticus


Section 6 Intracranial Trauma

58 Non-accidental Trauma

59 Depressed Skull Fracture

60 Growing Skull Fracture

61 Pneumolabyrinth Secondary to Trauma

62 Epidural Hematoma

63 Subdural Hematoma

64 Contusion

65 Coup-contre-coup Injuries

66 Diffuse Axonal Injury


Section 7 Intracranial Vascular Malformations: Congenital and Acquired

Subsection 7.1 Arterial malformations

67 Carotid Agenesis

68 Persistent Trigeminal Artery

69 Familial Intracranial Aneurysm

70 Saccular Aneurysm

71 Mycotic Aneurysm

72 Dolichoectasia of Basilar Artery

73 Moya Moya Disease

74 Carotid Artery Dissection

75 Carotid Artery Stenosis

76 Fibromuscular Dysplasia

77 Subclavian Steal Phenomenon

78 Arteriovenous Malformation

79 Dural Arteriovenous Fistula


Subsection 7.2 Venous and other vascular malformations

80 Developmental Venous Anomaly

81 Cavernous Angioma

82 Cavernous Hemangioma of Septum Pellucidum

83 Familial Cavernous Angiomas

84 Capillary Telangiectasias

85 Arachnoid Granulations in Venous Sinuses

86 Venous Sinus Thrombosis

87 Cortical Vein Thrombosis

88 Cavernous Sinus Thrombosis

89 Vein of Galen Malformation


Section 8 Stroke

90 Acute Arterial Infarction

91 Chronic Arterial Infarction

92 Lacunar Infarction

93 Watershed Infarction

94 Dyke-Davidoff-Masson Syndrome

95 Cerebral Autosomal Dominant Arteriopathy with Subcortical Infarcts and Leukoencephalopathy (CADASIL)

96 Vasculitis

97 Bechet's Syndrome

98 Global Anoxic Injury

99 Posterior Reversible Encephalopathy Syndrome

100 Venous Infarction

101 Brain Death


Section 9 Intracranial Hemorrhage

Subsection 9.1 Intraparenchymal Hemorrhage

102 Intraparenchymal Hematoma, Benign vs Malignant

103 Hemorrhagic Conversion of Infarction

104 Hypertensive Intraparenchymal Hemorrhage

105 Cerebral Amyloid Angiopathy

106 Remote Cerebellar Hemorrhage


Subsection 9.2 Subarachnoid Hemorrhage

107 Aneurysmal Subarachnoid Hemorrhage

108 Non-aneurysmal Subarachnoid Hemorrhage

109 Superficial Siderosis


Section 10 Hydrocephalus and Pneumocephalus

110 Medial diverticulum of Lateral Ventricle

111 Normal Pressure Hydrocephalus

112 Non-communicating Hydrocephalus

113 Shunt-related Complications

114 Tension Pneumocephalus


Section 11 Demyelinating Diseases

115 Multiple Sclerosis

116 Neuromyelitis Optica

117 Tumefactive Demyelinating Lesion

118 Susac's Syndrome

119 Marchiafava-Bignami Disease

120 Acute Disseminated Encephalomyelitis

121 Acute hemorrhagic encephalomyelitis


Section 12 Skull Lesions (Non-neoplastic)

122 Craniosynostosis

123 Bilateral Parietal Thinning


Section 13 Intracranial Tumors

Subsection 13.1 Tumors (and Tumor-Like Lesions) of the Scalp, Skull and Cranial nerves

124 Scalp Metastasis

125 Fibrous Dysplasia

126 Paget's Disease

127 Osteoma

128 Calvarial Hemangioma

129 Intradiploic Epidermoid

130 Ecchordosis Physaliphora

131 Clival Chordoma

132 Chondrosarcoma

133 Neuroblastoma Metastasis

134 Intraosseous Meningioma

135 Calvarial Metastasis

136 Schwannoma

137 Facial Nerve Hemangioma

138 Perineural Spread of Tumor


Subsection 13.2 Tumors (and Tumor-like Lesions) of the meninges

139 Intracranial Meningioma

140 Intracranial Lipoma

141 Hemangiopericytoma

142 Meningeal (Dura and Leptomeningeal) Metastasis

143 Hypertrophic Pachymeningitis


Subsection 13.3 Lymphoma and Germ Cell Tumors

144 Primary Central Nervous System Lymphoma

145 AIDS-Related Lymphoma

146 Secondary Central Nervous System Lymphoma

147 Intravascular Lymphoma

148 Post-transplant Lymphoproliferative Disorder

149 Granulocytic Sarcoma

150 Germinoma

151 Teratoma


Subsection 13.4 Tumors (and Tumor-like Lesions) of the Sella and Suprasellar compartment

152 Pituitary Microadenoma

153 Diabetes Insipidus

154 Pituitary Macroadenoma

155 Pituitary Apoplexy

156 Pituitary Carcinoma

157 Rathke Cleft Cyst

158 Sella Miscellaneous: Sheehan's syndrome

159 Craniopharyngioma

160 Langerhans Cell Histiocytosis of Pituitary Stalk

161 Lymphoc